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Western blot analysis of extracts of various cell lines, using Galactosidase alpha (Galactosidase alpha (GLA)) antibody (A1700) at 1:1000 dilution._Secondary antibody: HRP Goat Anti-Rabbit IgG (H+L) (AS014) at 1:10000 dilution._Lysates/proteins: 25ug per lane._Blocking buffer: 3% nonfat dry milk in TBST._Detection: ECL Enhanced Kit (RM00021)._Exposure time: 30s.
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Immunohistochemistry of paraffin-embedded human liver using Galactosidase alpha (Galactosidase alpha (GLA)) antibody (A1700) at dilution of 1:100 (40x lens).
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Immunohistochemistry of paraffin-embedded mouse kidney using Galactosidase alpha (Galactosidase alpha (GLA)) antibody (A1700) at dilution of 1:100 (40x lens).
Galactosidase alpha (GLA) Rabbit pAb
Catalog No：AB-A1700
Manufacturer：ABclonal
Synonyms：GLA;GALA
Applications：WB,IHC,IF
Reactivity：Human,Mouse
Host：Rabbit
Conjugate：No
€65,00 – €370,00
| Product Name: | Galactosidase alpha (GLA) Rabbit pAb |
| Category: | Polyclonal Antibodies |
| Description: | This gene encodes a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties. |
| Immunogen: | Recombinant fusion protein containing a sequence corresponding to amino acids 150-429 of human Galactosidase alpha (Galactosidase alpha (GLA)) (NP_000160.1). |
| Gene ID: | 2717 |
| Swiss prot: | P06280 |
| Molecular weight: | 48kDa |
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