Western blot analysis of extracts of various cell lines, using GAA antibody (A19234) at 1:1000 dilution.|Secondary antibody: HRP Goat Anti-Rabbit IgG (H+L) (AS014) at 1:10000 dilution.|Lysates/proteins: 25ug per lane.|Blocking buffer: 3% nonfat dry milk in TBST.|Detection: ECL Basic Kit (RM00020).|Exposure time: 10s.
GAA Rabbit mAb
Catalog No:AB-A19234
Manufacturer:ABclonal
Synonyms:GAA; LYAG; glucosidase alpha, acid
Applications:WB
Reactivity:Human,Mouse,Rat
Host:Rabbit
Conjugate:No
€65,00 – €485,00
Product Name: | GAA Rabbit mAb |
Category: | Monoclonal Antibodies |
Description: | This gene encodes lysosomal alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. The encoded preproprotein is proteolytically processed to generate multiple intermediate forms and the mature form of the enzyme. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe’s disease, which is an autosomal recessive disorder with a broad clinical spectrum. Alternative splicing results in multiple transcript variants. |
Immunogen: | Recombinant protein of human GAA. |
Gene ID: | 2548 |
Swiss prot: | P10253 |
Molecular weight: | 120,100,75kDa |
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