Western blot analysis of extracts of various cell lines, using GAA antibody (A7674) at 1:1000 dilution.|Secondary antibody: HRP Goat Anti-Rabbit IgG (H+L) (AS014) at 1:10000 dilution.|Lysates/proteins: 25ug per lane.|Blocking buffer: 3% nonfat dry milk in TBST.|Detection: ECL Basic Kit (RM00020).|Exposure time: 10s.
GAA Rabbit pAb
Catalog No:AB-A7674
Manufacturer:ABclonal
Synonyms:GAA;LYAG
Applications:WB,IF,IP
Reactivity:Human,Mouse,Rat
Host:Rabbit
Conjugate:No
€65,00 – €370,00
Product Name: | GAA Rabbit pAb |
Category: | Polyclonal Antibodies |
Description: | This gene encodes lysosomal alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. The encoded preproprotein is proteolytically processed to generate multiple intermediate forms and the mature form of the enzyme. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe’s disease, which is an autosomal recessive disorder with a broad clinical spectrum. Alternative splicing results in multiple transcript variants. |
Immunogen: | A synthetic peptide corresponding to a sequence within amino acids 350-450 of human GAA (NP_000143.2). |
Gene ID: | 2548 |
Swiss prot: | P10253 |
Molecular weight: | 105kDa |
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